Anantheswar Y N, Venkataramana N K
Department of Plastic Surgery, Manipal Hospital, Kengeri, Bangalore, India.
J Pediatr Neurosci. 2009 Jul;4(2):86-99. doi: 10.4103/1817-1745.57327.
Craniostenosis is a disease characterized by untimely fusion of cranial sutures resulting in a variety of craniofacial deformities and neurological sequelae due to alteration in cranial volume and restriction of brain growth. This involves vault sutures predominantly, but cranial base is not immune. Association with a variety of syndromes makes the management decision complex. These children need careful evaluation by multiple specialists to have strategic treatment options. Parental counseling is an important and integral part of the treatment. Recent advancements in the surgical techniques and concept of team approach have significantly enhanced the safety and outcome of these children. We had an opportunity of treating 57 children with craniostenosis in the last 15 years at our craniofacial service. Out of them, 40 were nonsyndromic and 17 were syndromic variety. We describe our successful results along with individualized operative technical modifications adopted based on the current understanding of the disease.
颅缝早闭是一种以颅缝过早融合为特征的疾病,由于颅腔容积改变和脑生长受限,导致各种颅面畸形和神经后遗症。这主要涉及颅顶缝,但颅底也不能幸免。与多种综合征相关使得治疗决策变得复杂。这些患儿需要多位专家进行仔细评估,以制定出合理的治疗方案。家长咨询是治疗的重要且不可或缺的一部分。手术技术和团队协作理念的最新进展显著提高了这些患儿治疗的安全性和效果。在过去15年里,我们的颅面外科有机会治疗了57例颅缝早闭患儿。其中,40例为非综合征型,17例为综合征型。我们将介绍我们的成功结果,以及基于对该疾病的当前认识所采用的个体化手术技术改进。