Bendadi Fatiha, van Tijn David A, Pistorius Lou, Freund Matthias W
Department of Pediatrics, Meander Medical Centre, Amersfoort, The Netherlands.
Pediatr Cardiol. 2012 Jan;33(1):188-91. doi: 10.1007/s00246-011-0114-6. Epub 2011 Sep 10.
Chiari's network is a remnant of the eustachian valve located in the right atrium. Incomplete involution of the fetal sinus venosus valves results in "redundant" Chiari's network, which may compromise cardiovascular function. This report describes a case with the novel finding of prenatal compromise due to redundant Chiari's network and an uncommon case with significant postnatal symptoms. In both cases, the symptoms (fetal hydrops and postnatal cyanosis) resolved spontaneously. The variety of cardiovascular pathologies described in the literature is believed to be associated with persistence of a Chiari network. Knowledge about this not always harmless structure is important for perinatologists, pediatricians, and pediatric cardiologists alike. The clinical importance of this rare pathology is that prenatal counseling may anticipate a generally positive outcome and that surgical intervention generally should be avoided.
奇阿里网是位于右心房的咽鼓管瓣遗迹。胎儿静脉窦瓣膜的不完全退化导致“多余的”奇阿里网，这可能会损害心血管功能。本报告描述了一例因多余的奇阿里网导致产前功能受损的新发现病例，以及一例产后出现明显症状的罕见病例。在这两个病例中，症状（胎儿水肿和产后发绀）均自发缓解。文献中描述的各种心血管病理情况被认为与奇阿里网的持续存在有关。了解这种并非总是无害的结构对围产医学专家、儿科医生和小儿心脏病专家同样重要。这种罕见病理情况的临床重要性在于，产前咨询可能预示总体预后良好，且一般应避免手术干预。
