Zheng Menghan, Chen Dong, Wang Jiaqi, Shang Jianfeng, Dong Fang
Department of Pathology, Beijing Anzhen Hospital, Capital Medical University, Beijing, China.
AME Case Rep. 2024 Apr 17;8:59. doi: 10.21037/acr-23-168. eCollection 2024.
Idiopathic cardiac osseous metaplasia in the right atrium of a 9-year-old boy, accompanied by right atrial Chiari network and right pulmonary artery embolism. This case is rare and can easily be misdiagnosed.
We encountered a case of a 9-year-old boy with a 3.5 cm diameter neoplasm in the right atrium. Preoperative imaging diagnosis could not determine the nature of the tumor, and the initial clinical suspicion of cardiac myxoma. After admission, a cardiotomy to remove foreign bodies and a pulmonary artery thrombectomy were performed.
Idiopathic cardiac osseous metaplasia is relatively rare, and it is even rarer to be accompanied by a Chiari network in the right atrium. Due to the location and characteristics of the lesion in this case, it is easy to be misdiagnosed as atrial myxoma in clinical practice. Whether it is idiopathic osseous metaplasia or myxoma, it needs to be performed surgical treatment and pathological examination can easily rule out the diagnosis of myxoma. However, as idiopathic cardiac metaplasia is difficult to encounter in clinical work and there are few reports in the literature, clinicians and pathologists need to consult more relevant literature. Learn to understand and master the disease through multi-party consultation.
一名9岁男孩右心房特发性心脏骨化生，伴有右心房奇静脉网和右肺动脉栓塞。该病例罕见，易被误诊。
我们遇到一例9岁男孩，右心房有一个直径3.5厘米的肿瘤。术前影像学诊断无法确定肿瘤性质，最初临床怀疑为心脏黏液瘤。入院后，进行了开胸取出异物和肺动脉血栓切除术。
特发性心脏骨化生相对罕见，伴有右心房奇静脉网则更为罕见。由于该病例病变的位置和特征，在临床实践中容易被误诊为心房黏液瘤。无论是特发性骨化生还是黏液瘤，都需要进行手术治疗，病理检查可轻易排除黏液瘤的诊断。然而，由于特发性心脏化生在临床工作中难以遇到且文献报道较少，临床医生和病理医生需要查阅更多相关文献，通过多方会诊来了解和掌握该疾病。
