Ji Yi, Xu Bing, Wang Xuejun, Liu Wenying, Chen Siyuan
Department of Pediatric Surgery & Center of Children Medicine, Sichuan Academy of Medical Sciences, Chengdu, China.
J Cardiothorac Surg. 2011 Sep 28;6:119. doi: 10.1186/1749-8090-6-119.
Plexiform neurofibromas are benign tumors originating from subcutaneous or visceral peripheral nerves, which are usually associated with neurofibromatosis type 1. They are almost always congenital lesions and often cause the surrounding soft tissue and bone to grow aberrantly. We treated a 12-year-old boy who presented with asymmetric pectus excavaum and an anterior chest wall plexiform neurofibroma. The pectus excavaum was corrected by modified Nuss procedure, followed by simultaneous resection of the giant mass. The patient is doing well at the 4 years follow-up visit.
丛状神经纤维瘤是起源于皮下或内脏周围神经的良性肿瘤，通常与1型神经纤维瘤病相关。它们几乎都是先天性病变，常导致周围软组织和骨骼异常生长。我们治疗了一名12岁男孩，他患有不对称漏斗胸和前胸壁丛状神经纤维瘤。通过改良努斯手术矫正漏斗胸，随后同时切除巨大肿块。在4年的随访中，患者情况良好。
