Department of Pediatrics, Taipei Veterans General Hospital, Taipei, Taiwan, ROC.
J Chin Med Assoc. 2012 Feb;75(2):87-90. doi: 10.1016/j.jcma.2011.12.004. Epub 2012 Jan 30.
Pulmonary hypoplasia is a rare but usually lethal disease. We report a full-term male neonate who presented with respiratory failure immediately after birth. Chest X-ray revealed a small lung volume despite advanced ventilator support. Respiratory failure persisted and this baby died at 40.5 hours of age. The autopsy showed a lung-to-birth weight ratio of 0.69% and a radial alveoli count of 2.97. All this information confirmed the diagnosis of primary congenital pulmonary hypoplasia.
肺发育不全是一种罕见但通常致命的疾病。我们报告了一例足月男性新生儿，出生后立即出现呼吸衰竭。尽管给予了高级呼吸机支持，胸部 X 线仍显示肺容量小。呼吸衰竭持续存在，该婴儿在出生后 40.5 小时死亡。尸检显示肺与出生体重比为 0.69%，肺泡计数为 2.97。所有这些信息都证实了原发性先天性肺发育不全的诊断。
