Espinosa Vicente, Martin-Achard Alec, Guinand Olivier
Service de médecine interne générale, HUG, 1211 Genève 14.
Rev Med Suisse. 2012 May 23;8(342):1125-9.
A 38 year old woman with a medical history of left pleurectomy and thoracic duct ligation for a recurrent chylothorax at age 21 was hospitalized for evaluation and treatment of a right sided pleural effusion and a pericardial effusion. A diffuse pulmonary lymphangiomatosis was diagnosed based on evidence obtained from a thoracic CT scan and from pleural and pericardial biopsies. The patient underwent drainage of these effusions and received systemic corticosteroids. Although both effusions initially recurred and required subsequent drainage and treatment by colchicine, evolution at 19 months of diagnosis is favorable. This case illustrates the fact that the prognosis of diffuse pulmonary lymphangiomatosis in adults may be characterized by a less aggressive evolution and by a more favorable prognosis than that observed in children.
一名38岁女性，21岁时因复发性乳糜胸接受过左侧胸膜切除术和胸导管结扎术，此次因右侧胸腔积液和心包积液入院评估及治疗。根据胸部CT扫描以及胸膜和心包活检结果诊断为弥漫性肺淋巴管瘤病。患者接受了这些积液的引流，并接受了全身性皮质类固醇治疗。尽管两种积液最初均复发，随后需要再次引流并用秋水仙碱治疗，但诊断后19个月的病情进展良好。该病例表明，与儿童相比，成人弥漫性肺淋巴管瘤病的预后可能表现为病情进展较缓和，预后更良好。
