Patankar A P, Sheth J H
Department of Neurosurgery, Baroda Medical College and SSG Hospital, & Neurosurgical Hospital, Vadodara, Gujarat, India.
Asian J Neurosurg. 2012 Apr;7(2):81-3. doi: 10.4103/1793-5482.98651.
Intramedullary dermoid cysts are rare tumors, especially those not associated with spinal dysraphism. Only six cases have been reported in the literature. Of these, only two cases have had magnetic resonance imaging studies. We report a case of an 18-year-old female patient, who presented with progressive weakness of both the lower limbs and wasting of both the upper limbs. Magnetic resonance imaging (MRI) showed an intramedullary lesion extending from C3 to D2 with peripheral enhancement on contrast. Decompression of the cystic contents with partial removal of cyst wall was done. Hair with oily cholesterol and keratin debris was encountered. Histopathology confirmed the diagnosis of dermoid cyst. This case adds to the previous reported cases of the rare and uncommon intramedullary space occupying lesions of the spinal cord.
髓内皮样囊肿是罕见肿瘤,尤其是那些与脊髓发育异常无关的肿瘤。文献中仅报道过6例。其中仅有2例进行了磁共振成像研究。我们报告1例18岁女性患者,其表现为双下肢进行性无力和双上肢萎缩。磁共振成像(MRI)显示一个从C3延伸至D2的髓内病变,增强扫描后周边强化。对囊肿内容物进行减压并部分切除囊肿壁。术中发现有毛发、油性胆固醇和角蛋白碎屑。组织病理学确诊为皮样囊肿。该病例补充了既往报道的罕见且不常见的脊髓髓内占位性病变病例。