Institute of Pathology, University of Sarajevo, Čekaluša, Sarajevo, Bosnia and Herzegovina.
Bosn J Basic Med Sci. 2012 Aug;12(3):203-6. doi: 10.17305/bjbms.2012.2485.
Interdigitating dendritic cell sarcoma is extremely rare neoplasm that mainly occurs in the lymph nodes. Only 45 cases have been reported in the literature to date. We report a case of this sarcoma arising from the liver and lung, a previosly unreported site for this neoplasm. An 19-year-old girl deteriorated rapidly after artificial abortion and died 4 weeks later. Autopsy showed markedly enlarged liver and lung with numerous nodules up to 0.5 centimeters in diameter. Microscopically, nodules was composed of large pleomorphic cells that were immunohistochemically positive for proteins S-100 and vimentin, some of them expressed positivity to fascin and CD 68, with a rich small CD3 positive T lymphocytic infiltrateite around them. Based of these findings, the present case was diagnosed as interdigitating dendritic cell sarcoma, a neoplasm that remains a diagnostic and clinical challenge, because it can mimic a wide variety of other malignant tumors and tumor-like lesions.
指状突树突细胞肉瘤是一种极为罕见的肿瘤,主要发生在淋巴结。迄今为止,文献中仅报道了 45 例。我们报告了一例发生于肝脏和肺部的该肉瘤,这是该肿瘤以前未报道过的部位。一名 19 岁女孩在人工流产后迅速恶化,并在 4 周后死亡。尸检显示肝脏和肺部明显肿大,有许多直径达 0.5 厘米的结节。显微镜下,结节由大而异型的细胞组成,这些细胞免疫组化表达 S-100 和波形蛋白阳性,其中一些表达 fascin 和 CD68 阳性,周围有丰富的小 CD3 阳性 T 淋巴细胞浸润。根据这些发现,本例诊断为指状突树突细胞肉瘤,该肿瘤仍然是一个诊断和临床挑战,因为它可以模仿多种其他恶性肿瘤和肿瘤样病变。