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以巨大脾梗死为表现的结节病

Sarcoidosis presenting as massive splenic infarction.

作者信息

Patel Ishita, Ismajli Mediola, Steuer Alan

机构信息

Rheumatology Department, Wexham Park Hospital, Heatherwood and Wexham Park Hospitals NHS Foundation Trust, Wexham, Slough, Berkshire SL2 4HL, UK.

出版信息

Case Rep Rheumatol. 2012;2012:834758. doi: 10.1155/2012/834758. Epub 2012 Jul 30.

Abstract

Sarcoidosis is a multisystem granulomatous disease of unknown aetiology. Granulomatous inflammation involving the spleen is common and associated with splenomegaly. However, massive splenomegaly is a rare occurrence. Infrequently massive splenomegaly can result in splenic infarction. Massive splenic infarction in sarcoidosis has, to our knowledge, not been previously reported. We present a case of a woman presenting with massive splenic infarction and sarcoidosis confirmed by granulomatous inflammation of the liver.

摘要

结节病是一种病因不明的多系统肉芽肿性疾病。累及脾脏的肉芽肿性炎症很常见,并与脾肿大相关。然而,巨大脾肿大是一种罕见的情况。巨大脾肿大很少会导致脾梗死。据我们所知,此前尚未有结节病伴巨大脾梗死的报道。我们报告一例女性患者,其表现为巨大脾梗死,且经肝脏肉芽肿性炎症证实患有结节病。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fba2/3420793/3b718681419a/CRIM.RHEUMATOLOGY2012-834758.001.jpg

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