Mellas Soufiane, Bouchikhi Ahmed Amine, Tazi Mohamed-Fadl, Khallouk Abdelhak, Elammari Jallal-Eddin, El Fassi Mohamed-Jamal, Mellas Naoufal, Farih Moulay Hassan
Department of Urology, Hassan II University Hospital of Fez, Fez 30020, Morocco ; Department of Anatomy, Faculty of Medicine of Fez, Fez, Morocco.
Case Rep Urol. 2012;2012:862493. doi: 10.1155/2012/862493. Epub 2012 Nov 19.
Undifferentiated pleomorphic sarcoma is known as a soft tissue sarcoma. Very few cases of this tumor originating from the renal parenchyma or renal capsule have been reported. We report a case of a 70-year-old patient admitted for enormous ureterohydronephrosis and pyelonephritis due to a pelvic ureter lithiasis. After draining by ureteral double J catheter, a nephroureterectomy was performed for nonfunctional kidney confirmed by scintigraphy. The histopathological study shows a pleomorphic undifferentiated sarcoma. The patient was sent to oncologists. Chemotherapy was proposed but the family decided to stop the treatment. The patient passed away 10 months later. Clinicians and pathologists should be aware of the very low occurrence of this renal tumor, which is extremely rare. Currently there is no consensus about its management. Our case extends the literature concerning this tumor.
未分化多形性肉瘤是一种软组织肉瘤。起源于肾实质或肾包膜的这种肿瘤病例报道极少。我们报告一例70岁患者，因盆腔输尿管结石导致巨大输尿管积水和肾盂肾炎入院。经输尿管双J管引流后，对经闪烁扫描证实无功能的肾脏进行了肾输尿管切除术。组织病理学研究显示为多形性未分化肉瘤。该患者被转至肿瘤学家处。建议进行化疗，但家属决定停止治疗。患者10个月后去世。临床医生和病理学家应意识到这种肾肿瘤的发生率极低，极为罕见。目前对于其治疗尚无共识。我们的病例扩展了关于这种肿瘤的文献。
