Fujita Kishu, Hata Mitsumasa, Sezai Akira, Minami Kazutomo
Department of Cardiovascular Surgery, Kitakanto Jyunkanki Hospital, 740 Shimohakoda, Hokkitsumachi, Shibukawa, Gunma, 377-0061, Japan,
Surg Today. 2014 May;44(5):948-51. doi: 10.1007/s00595-013-0511-y. Epub 2013 Feb 14.
A 59-year-old female underwent surgery for a primary malignant pericardial mesothelioma. She presented with progressive dyspnea, and several imaging studies demonstrated a 65 × 22 mm tumor in the aortopulmonary window, accompanied by massive pericardial effusion. The tumor was successfully excised with clean surgical margins under cardiopulmonary bypass, followed by patch reconstruction of the pulmonary artery, and was diagnosed as an epithelioid type of malignant pericardial mesothelioma. The patient tolerated the operation and subsequent adjuvant chemotherapy without any complications. She remained alive and asymptomatic for almost 3 years after surgery, despite the fact that the median survival of this disease is 6-10 months. This patient is the second longest postoperative survivor of this extremely rare, aggressive neoplasm.
一名59岁女性因原发性恶性心包间皮瘤接受手术。她表现为进行性呼吸困难，多项影像学检查显示在主肺动脉窗有一个65×22毫米的肿瘤，并伴有大量心包积液。在体外循环下肿瘤被成功切除，手术切缘干净，随后进行了肺动脉补片重建，诊断为上皮样型恶性心包间皮瘤。患者耐受了手术及后续辅助化疗，未出现任何并发症。尽管该疾病的中位生存期为6至10个月，但患者术后存活且无症状近3年。该患者是这种极其罕见、侵袭性肿瘤术后存活时间第二长的患者。
