Tural Deniz, Selçukbiricik Fatih, Günver Feray, Karışmaz Abdülkadir, Serdengecti Süheyla
Division of Medical Oncology, Department of Internal Medicine, Cerrahpasa Medical Faculty, Istanbul University, TR-34098 Istanbul, Turkey.
Case Rep Oncol Med. 2013;2013:907980. doi: 10.1155/2013/907980. Epub 2013 Feb 13.
First described by Hirsch and Helwig in 1961, chondroid syringomas (CSs) are rare, benign tumors of the skin arising from the eccrine sweat glands with tumor differentiation in the epithelial and mesenchymal tissues. They most commonly occur in the head and neck, although they may be also found in the axilla, trunk, limbs, and genitalia. The incidence of CS is <0.01% of all primary skin tumors. Malingnant chondroid syringomas (MCS), which are also called malignant mixed tumors of the skin, are extremely uncommon. MCSs commonly involve the limbs and rarely head and neck. In this article, we present a case of malignant chondroid syringoma localized in the face at the left nasolabial region in the light of literature review.
软骨样汗腺螺旋瘤(CSs)于1961年首次由 Hirsch 和 Helwig 描述,是一种罕见的皮肤良性肿瘤,起源于外分泌汗腺,具有上皮组织和间叶组织的肿瘤分化。它们最常发生在头颈部,不过也可能出现在腋窝、躯干、四肢和生殖器部位。CS 的发病率在所有原发性皮肤肿瘤中<0.01%。恶性软骨样汗腺螺旋瘤(MCS),也称为皮肤恶性混合瘤,极为罕见。MCS 通常累及四肢,很少累及头颈部。在本文中,我们结合文献复习,报道一例位于左侧鼻唇沟区域面部的恶性软骨样汗腺螺旋瘤病例。