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放射治疗作为辅助治疗在恶性软骨样汗腺癌淋巴结转移中的作用

The Role of Radiation Therapy as an Adjuvant Treatment in Nodal Metastasis of Malignant Chondroid Syringoma.

作者信息

Favareto Sergio L, Pellizzon Antonio Cassio A, Lopes Pinto Clóvis A, Bertolli Eduardo, Castro Douglas G

机构信息

Radiation Oncology, Antônio Cândido de Camargo Cancer Center, São Paulo, BRA.

Anatomic Pathology, Antônio Cândido de Camargo Cancer Center, São Paulo, BRA.

出版信息

Cureus. 2020 Nov 6;12(11):e11360. doi: 10.7759/cureus.11360.

DOI:10.7759/cureus.11360
PMID:33304693
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7720919/
Abstract

Malignant chondroid syringomas (MCSs) are extremely rare and aggressive skin tumors, and wide surgical excision is the main treatment. They can progress with local recurrence and nodal and distant metastasis. The role of radiotherapy is uncertain, but may enhance local control after surgical approach. We report a case of a 60-year-old female with this disease that, four years after surgical resection, presented with nodal metastasis and was managed with surgery and adjuvant radiotherapy.

摘要

恶性软骨样汗腺螺旋瘤(MCSs)是极其罕见且具有侵袭性的皮肤肿瘤,广泛手术切除是主要治疗方法。它们可进展为局部复发以及淋巴结和远处转移。放疗的作用尚不确定,但可能在手术治疗后增强局部控制。我们报告一例60岁患有此病的女性病例,该患者在手术切除四年后出现淋巴结转移,接受了手术及辅助放疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5c7/7720919/d519081532e4/cureus-0012-00000011360-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5c7/7720919/55a817ec9cf4/cureus-0012-00000011360-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5c7/7720919/0ef32f05d23e/cureus-0012-00000011360-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5c7/7720919/d519081532e4/cureus-0012-00000011360-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5c7/7720919/55a817ec9cf4/cureus-0012-00000011360-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5c7/7720919/0ef32f05d23e/cureus-0012-00000011360-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5c7/7720919/d519081532e4/cureus-0012-00000011360-i03.jpg

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本文引用的文献

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A rare large cutaneous chondroid syringoma involving a toe: A case report.一例累及脚趾的罕见大型皮肤软骨样汗腺腺瘤:病例报告
Medicine (Baltimore). 2018 Feb;97(5):e9825. doi: 10.1097/MD.0000000000009825.
2
Malignant chondroid syringoma in a West African cancer institute: A case report.西非癌症研究所的恶性软骨样汗腺癌:一例报告
Int J Surg Case Rep. 2016;25:137-8. doi: 10.1016/j.ijscr.2016.06.029. Epub 2016 Jun 23.
3
Adjuvant lymph-node field radiotherapy versus observation only in patients with melanoma at high risk of further lymph-node field relapse after lymphadenectomy (ANZMTG 01.02/TROG 02.01): 6-year follow-up of a phase 3, randomised controlled trial.
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Lancet Oncol. 2015 Sep;16(9):1049-1060. doi: 10.1016/S1470-2045(15)00187-4. Epub 2015 Jul 20.
4
A rare case of malignant chondroid syringoma of scalp.一例罕见的头皮恶性软骨样汗腺螺旋瘤。
Indian Dermatol Online J. 2013 Jul;4(3):236-8. doi: 10.4103/2229-5178.115533.
5
Facial localization of malignant chondroid syringoma: a rare case report.恶性软骨样汗腺腺瘤的面部定位:一例罕见病例报告。
Case Rep Oncol Med. 2013;2013:907980. doi: 10.1155/2013/907980. Epub 2013 Feb 13.
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Malignant chondroid syringoma of the face with bone invasion.
Am J Dermatopathol. 2013 May;35(3):395-8. doi: 10.1097/DAD.0b013e318274393d.
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Malignant chondroid syringoma of the face: a first reported case.面部恶性软骨样汗腺腺瘤:首例报告病例。
Otolaryngol Head Neck Surg. 2005 Aug;133(2):305-7. doi: 10.1016/j.otohns.2004.09.139.
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