Department of Diagnostic Radiology, Princess Margaret Hospital, Laichikok, Hong Kong.
Hong Kong Med J. 2013 Apr;19(2):174-7.
We describe a 50-year-old man who first presented with multiple skin lesions which were characteristic of Degos' syndrome. The patient developed multiple episodes of abdominal pain. Some episodes resolved with conservative management, for others he underwent urgent operations for bowel perforations. The patient subsequently underwent extensive small bowel resection, but further systemic deterioration ensued and he died. The imaging findings of Degos' syndrome and the implications of pneumatosis intestinalis and pneumoperitoneum are discussed.
我们描述了一位 50 岁男性，他最初表现为多发性皮肤损伤，具有 Degos 综合征的特征。该患者出现多次腹痛。有些病例经保守治疗缓解，其他病例则因肠穿孔而行紧急手术。随后，患者接受了广泛的小肠切除术，但随后出现了进一步的全身恶化，最终死亡。讨论了 Degos 综合征的影像学表现以及肠积气和气腹的意义。
