Otani Kazuhiro, Noda Kentaro, Ukichi Taro, Kingetsu Isamu, Kurosaka Daitaro
Division of Rheumatology, Department of Internal Medicine, Jikei University School of Medicine.
Nihon Rinsho Meneki Gakkai Kaishi. 2013;36(2):115-21. doi: 10.2177/jsci.36.115.
We report a 39-year-old female admitted for fever. She showed physical findings of bilateral granulomatous uveitis, swelling of the bilateral parotid glands, and paralysis of the left second branch of the trigeminal nerve. Her chest X-ray showed evidence of bilateral hilar lymphadenopathy. We performed biopsy of her parotid gland, and leading to a diagnosis of noncaseating epithelioid granuloma characterized by lymphocyte and multinucleated giant cell invasion. Therefore, she was diagnosed with the abortive type of Heerfordt syndrome which is a subtype of sarcoidosis. This is the only case associated with paralysis of the trigeminal nerve without paralysis of facial nerves to be reported in Japan.
我们报告了一名因发热入院的39岁女性。她有双侧肉芽肿性葡萄膜炎、双侧腮腺肿大及左侧三叉神经第二支麻痹的体格检查结果。她的胸部X线显示双侧肺门淋巴结肿大。我们对她的腮腺进行了活检，诊断为以淋巴细胞和多核巨细胞浸润为特征的非干酪样上皮样肉芽肿。因此，她被诊断为赫福特综合征的顿挫型，这是结节病的一种亚型。这是日本报道的唯一一例伴有三叉神经麻痹而无面神经麻痹的病例。
