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成人双腔右心室:病例系列

Double-Chambered Right Ventricle in Adulthood: A Case Series.

作者信息

Malone Richard Joseph, Henderson Everett Randall, Wilson Zachary Ryan, McMullan Matthew R, Skelton Thomas N, Campbell William F, McMullan Michael R

机构信息

School of Medicine, University of Mississippi Medical Center, Jackson, Mississippi.

Department of Medicine, University of Mississippi Medical Center, Jackson, Mississippi.

出版信息

CASE (Phila). 2024 Mar 8;8(3Part A):202-209. doi: 10.1016/j.case.2023.12.012. eCollection 2024 Mar.

DOI:10.1016/j.case.2023.12.012
PMID:38524987
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC10954581/
Abstract

• DCRV is a rare cardiac anomaly leading to subvalvular RVOT obstruction. • DCRV is most frequently found in children but can occur in adults. • Adults with DCRV are often initially misdiagnosed. • Echocardiography is the first-line imaging modality to visualize this anomaly. • Providers should be aware of this condition and the associated image findings.

摘要

• 双腔右心室是一种导致瓣膜下右心室流出道梗阻的罕见心脏畸形。

• 双腔右心室最常见于儿童,但也可发生于成人。

• 患有双腔右心室的成人最初常被误诊。

• 超声心动图是可视化这种畸形的一线成像方式。

• 医疗人员应了解这种情况及相关的影像表现。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/344d28c9f027/gr11.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/cc0955bcc490/ga1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/cf96225653fc/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/a3cf5f66b37b/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/f27e55983e84/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/38690cb67d07/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/1468b3c6ec47/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/dc4d8c5ee17b/gr6.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/ae084fac8479/gr7.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/81fcde726d72/gr8.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/1f84e61cc108/gr9.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/5eef93793316/gr10.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/344d28c9f027/gr11.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/cc0955bcc490/ga1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/cf96225653fc/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/a3cf5f66b37b/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/f27e55983e84/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/38690cb67d07/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/1468b3c6ec47/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/dc4d8c5ee17b/gr6.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/ae084fac8479/gr7.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/81fcde726d72/gr8.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/1f84e61cc108/gr9.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/5eef93793316/gr10.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25b5/10954581/344d28c9f027/gr11.jpg

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本文引用的文献

1
Dynamic cardiac computed tomography characteristics of double-chambered right ventricle.双腔右心室的动态心脏 CT 特征。
Sci Rep. 2022 Nov 29;12(1):20607. doi: 10.1038/s41598-022-25230-1.
2
Isolated Double-Chambered Right Ventricle - A Rare Entity.孤立性双腔右心室——一种罕见病症。
J Cardiovasc Echogr. 2020 Jul-Sep;30(3):162-164. doi: 10.4103/jcecho.jcecho_36_20. Epub 2020 Nov 9.
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An (In)Significant Ventricular Septal Defect and/or Double-Chambered Right Ventricle: Are There Any Differences in Diagnosis and Prognosis in Adult Patients.
小型(或中型)室间隔缺损和/或双腔右心室:成年患者在诊断和预后方面是否存在差异?
Cardiology. 2016;134(3):375-80. doi: 10.1159/000444743. Epub 2016 Apr 26.
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Double-chambered right ventricle: a review.双腔右心室:综述。
Cardiovasc Pathol. 2013 Nov-Dec;22(6):417-23. doi: 10.1016/j.carpath.2013.03.004. Epub 2013 May 20.
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Isolated double-chambered right ventricle in a young adult.青年成人孤立性双腔右心室。
Korean Circ J. 2011 May;41(5):272-5. doi: 10.4070/kcj.2011.41.5.272. Epub 2011 May 31.
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The role of echocardiography in diagnosing double chambered right ventricle in adults.超声心动图在诊断成人右心室双腔心方面的作用。
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Double-chambered right ventricle presenting in adulthood.成人期出现的双腔右心室。
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Double-chambered right ventricle: echocardiographic features.双腔右心室:超声心动图特征
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