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[肥厚型心肌病患者的双腔右心室。病例报告]

[Double-chambered right ventricle in a patient with hypertrophic cardiomyopathy. A case report].

作者信息

Iroulart Juan María, Ferrero Joaquín, Blanco Rocío, Licht Roshan, Miceli Ana, Pellegrini María Natalia, Pérez de Arenaza Diego, Pizarro Rodolfo

机构信息

Servicio de Cardiología, Hospital Italiano de Buenos Aires, Ciudad Autónoma de Buenos Aires, Argentina. Servicio de Cardiología Hospital Italiano de Buenos Aires Ciudad Autónoma de Buenos Aires Argentina.

出版信息

Arch Peru Cardiol Cir Cardiovasc. 2025 Feb 12;6(1):49-53. doi: 10.47487/apcyccv.v6i1.440. eCollection 2025 Jan-Mar.

DOI:10.47487/apcyccv.v6i1.440
PMID:40376124
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12076761/
Abstract

We present the case of a 42-year-old male patient with a history of bilateral lung transplantation and chronic graft dysfunction. The patient presented to the adult emergency department due to acute heart failure. During his stay in the emergency room and in outpatient follow-up, cardiac multi-imaging led to the diagnosis of double-chambered right ventricle with associated hypertrophic cardiomyopathy. Given the presence of advanced lung disease and poor adherence to immunosuppressant medication as well as clinical follow-ups, the patient was deemed unsuitable for re-lung transplantation. The optimization of his immunosuppressive medication was prioritized, and beta-blockers were added as part of the treatment for dynamic right ventricular outflow obstruction. He was referred to pulmonary rehabilitation, currently showing a partially favorable evolution to functional class II.

摘要

我们报告了一例42岁男性患者,有双侧肺移植及慢性移植物功能障碍病史。该患者因急性心力衰竭就诊于成人急诊科。在其留院急诊期间及门诊随访过程中,心脏多模态成像检查诊断为双腔右心室合并肥厚型心肌病。鉴于患者存在晚期肺部疾病、免疫抑制药物依从性差以及临床随访情况,认为其不适合再次进行肺移植。优先优化其免疫抑制药物治疗方案,并加用β受体阻滞剂作为治疗动态右心室流出道梗阻的一部分。他被转诊至肺康复治疗,目前功能分级部分改善至Ⅱ级。

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[Double-chambered right ventricle in a patient with hypertrophic cardiomyopathy. A case report].[肥厚型心肌病患者的双腔右心室。病例报告]
Arch Peru Cardiol Cir Cardiovasc. 2025 Feb 12;6(1):49-53. doi: 10.47487/apcyccv.v6i1.440. eCollection 2025 Jan-Mar.
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Case report: Double-chambered right ventricle diagnosed in a middle-aged female with hypertrophic cardiomyopathy and atrial flutter: A rare case.病例报告:一名患有肥厚型心肌病和心房扑动的中年女性被诊断为双腔右心室:罕见病例。
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本文引用的文献

1
2024 AHA/ACC/AMSSM/HRS/PACES/SCMR Guideline for the Management of Hypertrophic Cardiomyopathy: A Report of the American Heart Association/American College of Cardiology Joint Committee on Clinical Practice Guidelines.2024 AHA/ACC/AMSSM/HRS/PACES/SCMR 肥厚型心肌病管理指南:美国心脏协会/美国心脏病学会联合临床实践指南委员会的报告。
Circulation. 2024 Jun 4;149(23):e1239-e1311. doi: 10.1161/CIR.0000000000001250. Epub 2024 May 8.
2
Case report: Double-chambered right ventricle diagnosed in a middle-aged female with hypertrophic cardiomyopathy and atrial flutter: A rare case.病例报告:一名患有肥厚型心肌病和心房扑动的中年女性被诊断为双腔右心室:罕见病例。
Front Cardiovasc Med. 2022 Jul 22;9:937758. doi: 10.3389/fcvm.2022.937758. eCollection 2022.
3
Double-chambered right ventricle complicated by hypertrophic obstructive cardiomyopathy diagnosed as Noonan syndrome.右心室双腔并肥厚型梗阻性心肌病,诊断为努南综合征。
ESC Heart Fail. 2020 Apr;7(2):721-726. doi: 10.1002/ehf2.12650. Epub 2020 Feb 20.
4
Recurrent Hypotension During Hemodialysis Associated With Double Chamber Right Ventricle in Hypertrophic Cardiomyopathy.肥厚型心肌病合并双腔右心室患者血液透析期间反复出现的低血压
Circ J. 2018 Nov 24;82(12):3104-3105. doi: 10.1253/circj.CJ-17-1361. Epub 2018 May 31.
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2014 ESC Guidelines on diagnosis and management of hypertrophic cardiomyopathy: the Task Force for the Diagnosis and Management of Hypertrophic Cardiomyopathy of the European Society of Cardiology (ESC).2014年欧洲心脏病学会(ESC)肥厚型心肌病诊断和治疗指南:欧洲心脏病学会(ESC)肥厚型心肌病诊断和治疗工作组
Eur Heart J. 2014 Oct 14;35(39):2733-79. doi: 10.1093/eurheartj/ehu284. Epub 2014 Aug 29.
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Long-term natural history and postoperative outcome of double-chambered right ventricle--experience from two tertiary adult congenital heart centres and review of the literature.双腔右心室的长期自然病史及术后结局——来自两家三级成人先天性心脏病中心的经验及文献综述
Int J Cardiol. 2014 Jul 1;174(3):662-8. doi: 10.1016/j.ijcard.2014.04.177. Epub 2014 Apr 26.
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Double-chambered right ventricle: a review.双腔右心室:综述。
Cardiovasc Pathol. 2013 Nov-Dec;22(6):417-23. doi: 10.1016/j.carpath.2013.03.004. Epub 2013 May 20.
8
Outcomes of surgical repair of double-chambered right ventricle.双心室右心室修复术的结果。
Ann Thorac Surg. 2012 Jan;93(1):197-200. doi: 10.1016/j.athoracsur.2011.08.043. Epub 2011 Nov 16.
9
Echocardiographic assessment of right ventricular obstruction in hypertrophic cardiomyopathy.肥厚型心肌病右心室梗阻的超声心动图评估
Circ J. 2003 Oct;67(10):855-60. doi: 10.1253/circj.67.855.
10
Right ventricular involvement in hypertrophic cardiomyopathy: a case report and literature review.肥厚型心肌病的右心室受累:一例病例报告及文献综述
Clin Cardiol. 2001 Jan;24(1):2-8. doi: 10.1002/clc.4960240102.