Wang Chao, Miao Qi, Liu Xingrong, Li Xiaofeng
Department of Cardiac Surgery, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing, China.
J Card Surg. 2013 Jul;28(4):465-6. doi: 10.1111/jocs.12132. Epub 2013 Jun 14.
Left ventricular noncompaction (LVNC) is an uncommon genetic disorder of endocardial morphogenesis, which carries a high mortality from heart failure or sudden cardiac death. This condition is often first diagnosed in adults, but it has also been described in children with other cardiac anomalies. We discuss the management of a 10-year-old female with congenital aortic stenosis associated with LVNC.
左心室心肌致密化不全（LVNC）是一种罕见的心内膜形态发生遗传性疾病，因心力衰竭或心源性猝死导致的死亡率很高。这种疾病通常首次在成人中被诊断出来，但也有在伴有其他心脏异常的儿童中被描述的情况。我们讨论了一名患有与LVNC相关的先天性主动脉瓣狭窄的10岁女性的治疗。
