Ahmad Fateh, Evans Martin, White Nicholas, Nishikawa Hiroshi, Dover Stephen, Solanki Guirish, Rodrigues Desiderio
Craniofacial Unit, Birmingham Children's Hospital, Steelhouse Lane, Birmingham, West Midlands, B4 6NH, UK,
Childs Nerv Syst. 2014 Jan;30(1):177-9. doi: 10.1007/s00381-013-2202-9. Epub 2013 Jun 19.
Multisutural craniosynostosis as seen in Crouzon's syndrome can result in raised intracranial pressure, Chiari malformation (CM) and syringomyelia. Posterior calvarial distraction (PD) is a technique for addressing cranio-cephalic disproportion, and this case report describes the reversal of both CM and syrinx in a 6-year-old child who underwent PD initially for raise intracranial pressure.