表现为心力衰竭和壁内血栓形成的左心室心肌致密化不全。
Left ventricular non-compaction presenting with heart failure and intramural thrombus.
作者信息
Aryal Madan Raj, Badal Madan, Giri Smith, Pradhan Rajesh
机构信息
Department of Internal Medicine, Reading Health System, West Reading, Pennsylvania, USA.
出版信息
BMJ Case Rep. 2013 Jul 12;2013:bcr2013009757. doi: 10.1136/bcr-2013-009757.
Abstract
Left ventricular non-compaction (LVNC) is a rare disorder caused by the arrest of myocardial compaction during embryogenesis, leading to a non-compacted endocardial layer with marked trabeculations. The diagnosis is primarily based on echocardiographic demonstration of a spongy myocardium. Here, we present a young male with LVNC presenting with left heart failure and multiple left ventricular thrombi. We also review the presentation, diagnosis and management of this condition.
摘要
左心室心肌致密化不全（LVNC）是一种罕见的疾病，由胚胎发育过程中心肌致密化停滞引起，导致心内膜层未致密化并伴有明显的小梁形成。诊断主要基于超声心动图显示的海绵状心肌。在此，我们报告一名患有LVNC的年轻男性，其表现为左心衰竭和多个左心室血栓形成。我们还对该疾病的临床表现、诊断和治疗进行了综述。
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