Das Sakti Prasad, Ojha Niranjan, Ganesh G Shankar, Mohanty Ram Narayan
Department of Physical Medicine and Rehabilitation, SVNIRTAR, Olatpur, Cuttack District, Odisha, India.
Indian J Orthop. 2013 Jul;47(4):413-6. doi: 10.4103/0019-5413.114936.
Presence of single umbilical persistent vitelline artery distinguishes sirenomelia from caudal regression syndrome. We report a case of a12-year-old boy who had bilateral umbilical arteries presented with fusion of both legs in the lower one third of leg. Both feet were rudimentary. The right foot had a valgus rocker-bottom deformity. All toes were present but rudimentary. The left foot showed absence of all toes. Physical examination showed left tibia vara. The chest evaluation in sitting revealed pigeon chest and elevated right shoulder. Posterior examination of the trunk showed thoracic scoliosis with convexity to right. The patient was operated and at 1 year followup the boy had two separate legs with a good aesthetic and functional results.
单脐持续性卵黄动脉的存在可将并腿畸形与尾椎退化综合征区分开来。我们报告一例12岁男孩,其双侧脐动脉,双腿在小腿下三分之一处融合。双足发育不全。右脚有外翻摇椅底畸形。所有脚趾均存在但发育不全。左脚所有脚趾均缺失。体格检查显示左胫骨内翻。坐位胸部评估显示鸡胸和右肩抬高。躯干后部检查显示胸段脊柱侧弯,凸向右侧。该患者接受了手术,术后1年随访时,男孩拥有两条分开的腿,美观和功能效果良好。