Department of Ophthalmology, Centre Hospitalier Intercommunal de Créteil, University Paris-Est, Créteil, France.
Ophthalmologica. 2013;230(3):126-30. doi: 10.1159/000354111. Epub 2013 Aug 20.
To report unusual presentations of type 2A idiopathic macular telangiectasia (IMT).
A retrospective analysis of disease presentation was conducted in 32 patients with type 2A IMT. All patients underwent a complete ophthalmological examination, including spectral domain optical coherence tomography (SD-OCT), fluorescein angiography (FA) and indocyanine green angiography (ICGA).
Three out of 32 study patients showed the simultaneous presentation of type 2 IMT and other retinal diseases. In the first patient, the ophthalmological examination revealed a proliferative IMT associated with late-onset Stargardt disease. The second patient presented bilateral nonproliferative IMT and chronic serous chorioretinopathy in the left eye. The examination of the third patient revealed basal laminar drusen and soft drusen associated with IMT in both eyes.
Type 2 IMT may represent an unusual presentation of Stargardt disease, chronic serous chorioretinopathy and basal laminar drusen. These presentations are most likely coincidental and highlight the importance of FA, ICGA and SD-OCT in the diagnosis and treatment of such cases.
报告 2A 型特发性黄斑毛细血管扩张症（IMT）的不常见表现。
对 32 例 2A 型 IMT 患者的疾病表现进行回顾性分析。所有患者均接受全面眼科检查，包括谱域光学相干断层扫描（SD-OCT）、荧光素血管造影（FA）和吲哚青绿血管造影（ICGA）。
32 例研究患者中有 3 例同时出现 2 型 IMT 和其他视网膜疾病。在第一例患者中，眼科检查显示增殖性 IMT 伴有迟发性 Stargardt 病。第二例患者表现为双眼非增殖性 IMT 和左眼慢性浆液性脉络膜视网膜病变。第三例患者的检查显示双眼存在基底膜层内玻璃膜疣和软性玻璃膜疣，同时伴有 IMT。
2 型 IMT 可能是 Stargardt 病、慢性浆液性脉络膜视网膜病变和基底膜层内玻璃膜疣的不常见表现。这些表现很可能是偶然的，突出了 FA、ICGA 和 SD-OCT 在这些病例的诊断和治疗中的重要性。
