Nigam Arima, Trehan Vijay
1Department of Cardiology,GB Pant Hospital,New Delhi,India.
Cardiol Young. 2014 Oct;24(5):926-8. doi: 10.1017/S1047951113001406. Epub 2013 Sep 18.
Hemitruncus is a rare congenital heart disease. Anomalous origin of the left pulmonary artery is not only rare but also pathogenetically different from anomalous origin of the right pulmonary artery from the ascending aorta. In most cases in isolated hemitrucus pressures in the right ventricle and the normally originating pulmonary artery are systemic or suprasystemic. We present a rare case of anomalous origin of the left pulmonary artery from the ascending aorta diagnosed in an adult with normal pressures in the right ventricle and normally originating pulmonary artery. To the best of our knowledge, this unique haemodynamics has never been reported in the literature.
半侧心(动脉干)是一种罕见的先天性心脏病。左肺动脉异常起源不仅罕见,而且在发病机制上与右肺动脉从升主动脉异常起源不同。在大多数孤立性半侧心(动脉干)病例中,右心室和正常起源的肺动脉压力为体循环或高于体循环压力。我们报告了一例罕见的升主动脉起源的左肺动脉异常病例,该病例发生在一名右心室压力正常且肺动脉正常起源的成年人身上。据我们所知,这种独特的血流动力学情况在文献中从未有过报道。