Gupta Saurabh Kumar, Choubey Mrigank, Kumar Sanjeev, Patel Chetan, Airan Balram
Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India.
Department of Cardiovascular Radiology and Endovascular Interventions, All India Institute of Medical Sciences, New Delhi, India.
Ann Pediatr Cardiol. 2023 Jan-Feb;16(1):65-70. doi: 10.4103/apc.apc_98_22. Epub 2023 Apr 4.
The hemodynamics of anomalous origin of the pulmonary artery (PA) from the aorta is challenging. Different sources of blood supply to the lungs lead to a unique state of differential flow, pressure, and pulmonary vascular resistance in each lung. The decision for surgical reimplantation of the anomalous PA during infancy is easy. The assessment of operability beyond infancy, however, is perplexing. In this report, we describe stepwise multimodal hemodynamic evaluation and successful surgical management in a 15-year-old boy with an isolated anomalous origin of the right PA from the aorta. We also report 5-year hemodynamic data confirming sustained benefit over the long term, thus providing much-needed clinical validation of often cited Poiseuille's and Ohm's laws.
肺动脉（PA）起源于主动脉异常的血流动力学情况颇具挑战性。肺部不同的血液供应来源导致每个肺脏处于独特的分流、压力和肺血管阻力状态。婴儿期进行异常肺动脉手术再植入的决策较为容易。然而，对于婴儿期之后的手术可行性评估却令人困惑。在本报告中，我们描述了一名15岁男孩，其右肺动脉孤立性起源于主动脉，我们对其进行了逐步多模式血流动力学评估及成功的手术治疗。我们还报告了5年的血流动力学数据，证实了长期持续获益，从而为常被引用的泊肃叶定律和欧姆定律提供了急需的临床验证。
