Brown P, Jannotta F, Gibbs C J, Baron H, Guiroy D C, Gajdusek D C
Laboratory of CNS Studies, NINDS, National Institutes of Health, Bethesda, MD 20892.
Neurology. 1990 Feb;40(2):226-8. doi: 10.1212/wnl.40.2.226.
We report the case of a 73-year-old patient in whom a diagnosis of Creutzfeldt-Jakob disease, suggested by the clinical course, was verified by the neuropathologic finding of widespread spongiform change and astrogliosis, the presence of proteinase-resistant protein in brain extracts, and the experimental transmission of spongiform encephalopathy to primates inoculated with brain tissue. However, neuropathologic examination also revealed a profusion of senile and neuritic plaques and neurofibrillary tangles that reacted with antibody to the amyloid beta-protein characteristic of Alzheimer's disease, but not with antibody to the scrapie amyloid protein characteristic of Creutzfeldt-Jakob disease.
我们报告了一例73岁患者的病例。该患者临床病程提示为克雅氏病,经神经病理学检查发现广泛的海绵状改变和星形胶质细胞增生、脑提取物中存在蛋白酶抗性蛋白以及将海绵状脑病实验性传播给接种脑组织的灵长类动物而得以证实。然而,神经病理学检查还发现大量的老年斑和神经原纤维缠结,它们与针对阿尔茨海默病特征性β淀粉样蛋白的抗体发生反应,但与针对克雅氏病特征性瘙痒病淀粉样蛋白的抗体不发生反应。