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幼年性黄色肉芽肿:非皮肤疾病的多样表现

Juvenile xanthogranuloma: diverse presentations of noncutaneous disease.

作者信息

Murphy Joseph T, Soeken Tim, Megison Steve, Perez Eduardo

机构信息

*Department of Pediatric Surgery, Children's Medical Center, University of Texas Southwestern Medical Center, Dallas †Baylor College of Medicine, Baylor University School of Medicine, Houston, TX ‡Department of Pediatric Surgery, University of Miami, Coral Gables, FL.

出版信息

J Pediatr Hematol Oncol. 2014 Nov;36(8):641-5. doi: 10.1097/MPH.0000000000000027.

DOI:10.1097/MPH.0000000000000027
PMID:24065046
Abstract

Juvenile xanthogranulomas (JXGs) are benign cutaneous lesions of childhood that often spontaneously involute. They rarely present as a noncutaneous tumors. However, JXG tumors have been described in numerous noncutaneous anatomic sites, presenting with a variety of symptoms. The severity of symptoms and accurate preoperative diagnosis of JXG should determine operative and nonoperative treatment options of these uncommon, benign, and self-limiting tumors. We report 3 cases of symptomatic, noncutaneous JXG from disparate anatomic sites all treated with aggressive surgical resection.

摘要

幼年黄色肉芽肿(JXGs)是儿童期的良性皮肤病变,通常会自发消退。它们很少表现为非皮肤肿瘤。然而,JXGs肿瘤已在许多非皮肤解剖部位被描述,表现出各种症状。JXGs症状的严重程度和准确的术前诊断应决定这些罕见、良性且自限性肿瘤的手术和非手术治疗方案。我们报告了3例来自不同解剖部位的有症状的非皮肤JXGs病例,均采用积极的手术切除治疗。

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