Desai Soaham Dilip, Patel Dipen, Bharani Sheela, Kharod Nikhil
Department of Neuromedicine, Shree Krishna Hospital, Pramukhswami Medical College, Karamsad, Gujarat, India.
J Pediatr Neurosci. 2013 May;8(2):123-5. doi: 10.4103/1817-1745.117842.
We present a 9-year-old boy with history of perinatal asphyxia and neonatal seizures; who presented with delayed development of speech, with predominant dysarthria, dysphagia, and drooling of saliva and unable to protrude tongue along with delayed motor and mental milestones. He had complex partial seizures since last 3 years requiring multiple anti-epileptic drugs. He had dysarthria, nasal twang, and drooling of saliva with difficulty in chewing and swallowing. Hearing and understanding were normal. Bilateral trigemino-facio-linguo-pharyngeal palsy was noticed on voluntary movements with normal jaw jerk with preserved automatic and emotional motor movements. Electroencephalography revealed focal left fronto-temporal epileptiform discharges and brain imaging was suggestive of bilateral cortical and subcortical region encephalomalacia, predominantly involving bilateral opercular region. The clinical and neuroimaging features correspond to bilateral opercular syndrome which could have resulted from the perinatal insult in this case.
我们报告一名9岁男孩,有围产期窒息和新生儿惊厥病史;表现为言语发育迟缓,主要有构音障碍、吞咽困难和流涎,不能伸舌,同时运动和智力发育里程碑延迟。他在过去3年中患有复杂部分性癫痫发作,需要多种抗癫痫药物治疗。他有构音障碍、鼻音、流涎,咀嚼和吞咽困难。听力和理解能力正常。在自主运动时发现双侧三叉神经-面神经-舌咽神经麻痹,下颌反射正常,自动和情感运动保留。脑电图显示左侧额颞叶局灶性癫痫样放电,脑部影像学提示双侧皮质和皮质下区域脑软化,主要累及双侧岛盖区。临床和神经影像学特征符合双侧岛盖综合征,本例可能是由围产期损伤所致。