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孤立性右侧异常肺静脉连接伴显著右心室扩大及房间隔完整

Isolated Right Sided Anomalous Pulmonary Venous Connection Associated with Significant Right ventricular Enlargement and Intact Interatrial Septum.

作者信息

Ojaghi Haghigh Zahra, Sadeghpour Anita, Alizadehasl Azin

机构信息

Rajaie Cardiovascular Medical and Research Center, Tehran University of Medical Sciences, Tehran, Iran.

出版信息

J Cardiovasc Thorac Res. 2012;4(4):123-4. doi: 10.5681/jcvtr.2012.029. Epub 2012 Oct 30.

Abstract

Partial anomalous pulmonary venous connection (PAPVC) is a very rare congenital heart disease where one or more of the pulmonary veins are connected to the venous circulation. Although initially suspected with inexplicable right ventricular enlargement on transthoracic echocardiography, other modalities such as transesophageal echocardiography, CT angiography or cardiac Magnetic resonance (CMR) imaging are able to diagnosis the anatomical abnormalities. We present a 29-year-old female with moderate right ventricular enlargement and isolated right upper and middle pulmonary vein anomalous return to superior vena cava.

摘要

部分性肺静脉异位连接(PAPVC)是一种非常罕见的先天性心脏病,其中一条或多条肺静脉与静脉循环相连。虽然经胸超声心动图最初怀疑有无法解释的右心室扩大,但其他检查手段,如经食管超声心动图、CT血管造影或心脏磁共振(CMR)成像,能够诊断解剖学异常。我们报告一名29岁女性,有中度右心室扩大,孤立的右上和中叶肺静脉异常回流至上腔静脉。

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