Ohta Akiko, Nagai Masaki, Nishina Motoko, Tomimitsu Hiroyuki, Kohsaka Hitoshi
Department of Public Health, Saitama Medical University Faculty of Medicine , Saitama , Japan.
Mod Rheumatol. 2014 May;24(3):477-80. doi: 10.3109/14397595.2013.844308. Epub 2013 Oct 21.
To estimate the number of patients with polymyositis/dermatomyositis (PM/DM) in Japan and the prevalence rate and incidence rate of the disease.
The electronic database in the nationwide registration system on intractable diseases from 2003 to 2010 was utilized to identify the number of prevalent and incident cases of PM/DM. The electronic data entry rate was used to establish the total number of registered cases.
The estimated total number of patients with PM/DM and the prevalence rate in Japan in 2010 were 17,000 and 13.2 per 100,000 population, respectively. The prevalence of PM/DM ranged from 10 to 13 per 100,000 population with a trend toward increasing over time. The incidence of PM/DM was estimated within the range 10-13 per 1,000,000 person-years, except for 2003.
We report the prevalence and incidence of PM/DM recently in Japan for the first time at the nationwide population level. Because the prevalence seems to be increasing recently, continued monitoring of these epidemiologic features is required.
估算日本多发性肌炎/皮肌炎（PM/DM）患者的数量以及该病的患病率和发病率。
利用2003年至2010年全国难治性疾病登记系统中的电子数据库，确定PM/DM的现患病例数和新发病例数。采用电子数据录入率来确定登记病例的总数。
2010年日本PM/DM患者的估计总数和患病率分别为17,000例和每10万人中13.2例。PM/DM的患病率为每10万人中10至13例，且有随时间增加的趋势。除2003年外，PM/DM的发病率估计在每100万人年10 - 13例的范围内。
我们首次在全国人口水平上报告了日本近期PM/DM的患病率和发病率。由于患病率近期似乎在上升，因此需要持续监测这些流行病学特征。
