Eljebbouri Brahim, Gazzaz Miloudi, Akhaddar Ali, Elmostarchid Brahim, Boucetta Mohamed
Department of Neurosurgery, Med V University, Mohamed V Teaching Hospital, Rabat, Morocco.
Acta Med Iran. 2013;51(10):727-9.
Pediatric intramedullary schwannoma without neurofibromatosis is extremely rare with only five cases reported so far. We present this rare finding in an 10-year-old boy who presented with a sudden onset of weakness in the lower limbs. An intraoperative diagnosis of schwannoma enabled us to carry out a total excision of the tumor, which resulted in near complete recovery at 10 months follow-up. Although rare, this diagnosis should be considered when a child presents with a solitary intramedullary tumor since its total resection can be achieved improving surgical outcome.
无神经纤维瘤病的小儿髓内神经鞘瘤极为罕见,迄今为止仅报道过5例。我们在此报告一名10岁男孩的这一罕见病例,该男孩突然出现下肢无力。术中诊断为神经鞘瘤,这使我们能够对肿瘤进行全切,术后10个月随访时患儿近乎完全康复。尽管罕见,但当儿童出现孤立性髓内肿瘤时应考虑这一诊断,因为全切肿瘤可改善手术预后。