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常染色体显性遗传性多囊肾病患者的双侧乳头状肾细胞癌和肾血管平滑肌脂肪瘤:两例病例报告及文献复习

Bilateral papillary renal cell carcinoma and angiomyolipoma in the patients with autosomal dominant polycystic kidney disease: case report of two cases and literature review.

作者信息

Konosu-Fukaya S, Nakamura Y, Fujishima F, Kasajima A, Takahashi Y, Joh K, Ikeda Y, Ioritani N, Watanabe M, Sasano H

机构信息

Yasuhiro Nakamura MD, PhD, Department of Pathology, Tohoku University School of Medicine, 2-1 Seiryo-machi, Aoba-ku, Sendai, 980-8575 Japan, tel. +81-22-717-8050, fax +81-22-717-8051, e-mail:

出版信息

Pol J Pathol. 2013 Dec;64(4):303-7. doi: 10.5114/pjp.2013.39340.

Abstract

We herein report two rare cases of bilateral renal neoplasms associated with autosomal dominant polycystic kidney disease (ADPKD). Case 1: Bilateral nephrectomy was performed on bilateral renal masses in a 58-year-old man with ADPKD. Case 2: Bilateral nephrectomy was performed on bilateral renal masses in a 32-year-old man with clinically suspected ADPKD. In case 1, angiomyolipoma (AML) and papillary renal cell carcinoma (PRCC) (type 1) were detected in the bilateral kidneys. In case 2, PRCC (type 1) was detected in the bilateral kidneys.

摘要

我们在此报告两例与常染色体显性多囊肾病(ADPKD)相关的双侧肾肿瘤罕见病例。病例1:对一名58岁患有ADPKD的男性双侧肾肿块进行了双侧肾切除术。病例2:对一名32岁临床疑似患有ADPKD的男性双侧肾肿块进行了双侧肾切除术。在病例1中,双侧肾脏检测到血管平滑肌脂肪瘤(AML)和1型乳头状肾细胞癌(PRCC)。在病例2中,双侧肾脏检测到1型PRCC。

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