单节段肝内胆管多发纤维囊性病：3 例报告。

Monosegmental hepatobiliary fibropolycystic disease mimicking a mass: report of three cases.

机构信息

Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center, Daegu 700-712, Korea.

Department of Hepatobiliary Surgery, Keimyung University School of Medicine, Dongsan Medical Center, Daegu 700-712, Korea.

出版信息

Korean J Radiol. 2014 Jan-Feb;15(1):54-60. doi: 10.3348/kjr.2014.15.1.54. Epub 2014 Jan 8.

DOI:10.3348/kjr.2014.15.1.54

PMID:24497792

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3909862/

Abstract

Hepatobiliary fibropolycystic diseases are a unique group of entities involving the liver and biliary tract, which are caused by abnormal embryologic development of the ductal plates at various stages. We experienced strange hepatobiliary fibropolycystic diseases with a complex mass composed of malformed ducts and biliary cysts, which did not belong to, and were different from, previously known malformations. They were unique in imaging and histologic features. We herein report three cases of monosegmental hepatobiliary fibropolycystic disease mimicking a mass.

摘要

肝胆纤维多囊性疾病是一组独特的实体疾病，涉及肝脏和胆道，是由导管板在各个阶段的异常胚胎发育引起的。我们遇到了一种奇怪的肝胆纤维多囊性疾病，其复杂的肿块由畸形的胆管和胆管囊肿组成，既不属于也不同于以前已知的畸形。它们在影像学和组织学特征上是独特的。本文报告了 3 例单节段肝胆纤维多囊性疾病，表现为肿块。