Choi B I, Yeon K M, Kim S H, Han M C
Department of Radiology, College of Medicine, Seoul National University, Korea.
Radiology. 1990 Jan;174(1):161-3. doi: 10.1148/radiology.174.1.2294544.
Two adults with communicating cavernous ectasia of the biliary tract (Caroli disease) are described. Both patients had the pure form of the disease, characterized by saccular dilatation of intrahepatic bile ducts, multiple intrahepatic calculi, absence of portal hypertension, and associated cystic renal disease. Computed tomographic (CT) scans of the liver showed tiny dots with strong contrast enhancement within dilated intrahepatic bile ducts (the central dot sign). These intraluminal dots on CT scans corresponded to intraluminal portal veins on sonograms, findings indicating portal radicles surrounded by dilated intrahepatic bile ducts.
本文描述了两名患有交通性胆管海绵状扩张症（卡罗里病）的成年人。两名患者均为该病的单纯型，其特征为肝内胆管囊状扩张、多发肝内结石、无门静脉高压以及合并囊性肾病。肝脏计算机断层扫描（CT）显示，扩张的肝内胆管内有强化明显的微小点状影（中心点征）。CT扫描上的这些管腔内点状影在超声检查中对应于管腔内门静脉，这些表现提示门静脉分支被扩张的肝内胆管包绕。
