Buturak Ali, Saygili Ozlem, Ulus Sıla, Kalfa Melike, Karabulut Hasan, Alhan Cem, Dagdelen Sinan, Aksu Kenan
Department of Cardiology, Acıbadem University School of Medicine , Gülsuyu Mah. Fevzi Çakmak Cad. Divan Sok. No:1 Maltepe, Istanbul , Turkey.
Mod Rheumatol. 2014 May;24(3):532-6. doi: 10.3109/14397595.2013.874731. Epub 2014 Feb 18.
Behçet's disease is a multisystemic, chronic inflammatory disorder with diffuse clinical manifestations including the cardiovascular system. Endomyocardial fibrosis is a rarely seen complication of Behçet's disease leading to progressive heart failure. We report a case of right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a 26-year-old male Turkish patient with Behçet's disease, who had heart failure symptoms. In addition, the previously reported cases of endomyocardial fibrosis complicating Behçet's disease are reviewed in this article.
白塞病是一种多系统慢性炎症性疾病,临床表现多样,累及心血管系统。心内膜纤维化是白塞病罕见的并发症,可导致进行性心力衰竭。我们报告一例26岁患有白塞病的土耳其男性患者,出现心力衰竭症状,其右心室心内膜纤维化酷似埃布斯坦畸形。此外,本文还回顾了既往报道的白塞病并发心内膜纤维化的病例。