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白塞病与心血管受累:我们对白塞病无症状患者的经验。

Behcet's disease and cardiovascular involvement: our experience of asymptomatic Behcet's patients.

作者信息

Ulusan Zeynep, Karadag Ayse Serap, Tasar Mehmet, Kalender Mehmet, Darcin Osman Tansel

机构信息

Kecioren Research and Training Hospital, Ankara, Turkey.

Department of Dermatology, 100.yil University Medical School, Van, Turkey.

出版信息

Cardiovasc J Afr. 2014 Mar-Apr;25(2):63-6. doi: 10.5830/CVJA-2014-003.

Abstract

Behcet's syndrome is a systemic inflammatory disease associated with vasculitis, and arterial, venous and cardiac disorders. Thirty-eight Behcet's disease patients were examined prospectively with echocardiography, ultrasonography and computed tomography, and coagulation parameters were determined. Deep venous insufficiency was found in 16 patients, venous thrombosis in seven, one patient had iliac artery stenosis, three had carotid arterial intimal proliferation, two patients had aortic annulus dilatation, six had aortic valve insufficiency, and three had mitral valve insufficiency. None had coagulation defects. To decrease morbidity and mortality rates, a multidisciplinary approach is important for early diagnosis of cardiovascular involvement in Behcet's disease.

摘要

白塞病是一种与血管炎以及动脉、静脉和心脏疾病相关的全身性炎症性疾病。对38例白塞病患者进行了超声心动图、超声检查和计算机断层扫描的前瞻性检查,并测定了凝血参数。发现16例患者存在下肢深静脉功能不全,7例有静脉血栓形成,1例有髂动脉狭窄,3例有颈动脉内膜增生,2例有主动脉瓣环扩张,6例有主动脉瓣关闭不全,3例有二尖瓣关闭不全。所有患者均无凝血缺陷。为降低发病率和死亡率,多学科方法对于白塞病心血管受累的早期诊断很重要。

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