Kambakamba P, Lesurtel M, Breitenstein S, Emmert My, Wilhelm Mj, Clavien Pa
University Hospital of Zurich, Zurich, Switzerland.
J Surg Case Rep. 2012 Jun 1;2012(6):4. doi: 10.1093/jscr/2012.6.4.
A 34-year-old patient was scheduled for valve replacement to treat a symptomatic mitral regurgitation. The preoperative work-up incidentally discovered an intra-abdominal cystic tumour extending from the epigastrium to the pelvic region on a computed tomography scan. The patient had no abdominal symptoms by the giant cyst from unkown origin. An open "en bloc" resection disclosed a large cyst in the mesocolon. Pathological examination, including immunohistochemistry, enabled the diagnosis of a mesenteric cystic lymphangioma. Long-term follow-up of 12 months shows no recurrence. Mesenteric cystic lymphangioma, which is extremely rare in adults, is a challenge to diagnose and needs complete resection to ensure dignity and to avoid recurrence.
一名34岁患者计划进行瓣膜置换术以治疗有症状的二尖瓣反流。术前检查偶然在计算机断层扫描中发现一个从腹上区延伸至盆腔区域的腹腔囊性肿瘤。患者没有因这个不明来源的巨大囊肿而出现腹部症状。一次开放性“整块”切除显示在结肠系膜中有一个大囊肿。包括免疫组织化学在内的病理检查确诊为肠系膜囊性淋巴管瘤。12个月的长期随访显示无复发。肠系膜囊性淋巴管瘤在成人中极为罕见,诊断具有挑战性,需要完整切除以确保疗效并避免复发。