Tan Dominic Ti Ming, Chok Aik Yong, Farah Benjamin Livingston, Yan Yet Yen, Toh Ee-Lin
College of Medical and Dental Sciences, University of Birmingham, Birmingham, UK
Department of Surgery, Sandwell and West Birmingham Hospitals NHS Trust, Birmingham, UK.
BMJ Case Rep. 2019 Nov 24;12(11):e231037. doi: 10.1136/bcr-2019-231037.
Mesenteric lymphangiomas are relatively rare, with clinical symptoms ranging from an asymptomatic presentation to an acute abdomen. The natural history and biological behaviour of this entity can range from slow indolent lesions to aggressive tumours with a risk of malignant transformation. Spontaneous regression of a mesenteric lymphangioma is rare. We herein report a case of a jejunal mesenteric lymphangioma that was initially detected incidentally in an asymptomatic patient with a subsequent sudden increase in size with resulting surrounding mass effect after 9 months and a spontaneous partial regression at surgical resection. Our case is the first reported case which outlines a period in the natural history and evolution of microcystic mesenteric lymphangioma, illustrating the sudden enlargement likely attributable to spontaneous and self-limiting haemorrhage and subsequent partial regression at surgical resection. We thenceforth propose a possible management algorithm for adult patients with mesenteric lymphangiomas.
肠系膜淋巴管瘤相对罕见,临床症状从无症状表现到急腹症不等。该病变的自然病史和生物学行为范围从缓慢生长的惰性病变到有恶变风险的侵袭性肿瘤。肠系膜淋巴管瘤自发消退的情况罕见。我们在此报告一例空肠系膜淋巴管瘤病例,该病例最初在一名无症状患者中偶然发现,9个月后瘤体大小突然增加并产生周围肿块效应,手术切除时出现自发部分消退。我们的病例是首例报道的描述微囊性肠系膜淋巴管瘤自然病史和演变过程的病例,说明了瘤体突然增大可能归因于自发且自限性的出血,以及手术切除时随后的部分消退。因此,我们提出了一种针对成年肠系膜淋巴管瘤患者的可能的管理算法。