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皮质盲作为脑静脉血栓形成的一种罕见表现。

Cortical blindness as a rare presentation of cerebral venous thrombosis.

作者信息

Wang Bonnie, Moon Seong-Jin, Olivero William C, Wang Huan

机构信息

Department of Internal Medicine, University of Illinois, College of Medicine at Urbana-Champaign, Urbana, IL, USA Carle Foundation Hospital, Urbana, IL, USA

University of Illinois, College of Medicine at Urbana-Champaign, Urbana, IL, USA.

出版信息

J Surg Case Rep. 2013 May 9;2013(5):rjt035. doi: 10.1093/jscr/rjt035.

DOI:10.1093/jscr/rjt035
PMID:24964444
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3813509/
Abstract

Cerebral venous thrombosis (CVT) remains a diagnostic and therapeutic challenge for clinicians. Manifesting in a remarkably wide spectrum of symptoms and signs, CVT often presents in a misleading fashion-if unrecognized or misdiagnosed, it carries potentially fatal consequences. Visual loss is quite rare as the initial presentation of CVT and is typically a finding more frequent in chronic cases with associated papilledema on funduscopy Ferro, Lopes, Rosas and Fontes (Delay in Hospital Admission of Patients with Cerebral Vein and Dural Sinus Thrombosis. Cerebrovasc Dis 2005;19: :152-6). We report a rare case of acute cortical blindness as the initial presentation of CVT in an 18-year-old female patient and review the current literature.

摘要

脑静脉血栓形成(CVT)对临床医生来说仍然是一个诊断和治疗上的挑战。CVT的症状和体征表现极为多样,常常以误导性的方式呈现——如果未被识别或误诊,可能会带来致命后果。视力丧失作为CVT的初始表现相当罕见,通常在慢性病例中更常见,眼底镜检查可见相关视乳头水肿[费罗、洛佩斯、罗萨斯和丰特斯(脑静脉和硬脑膜窦血栓形成患者的住院延迟。脑血管疾病2005;19:152 - 6)]。我们报告一例罕见病例,一名18岁女性患者以急性皮质盲作为CVT的初始表现,并对当前文献进行综述。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7a28/3813509/63cb918ffc70/rjt03503.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7a28/3813509/0d94a8eea389/rjt03501.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7a28/3813509/0632c1da9dc7/rjt03502.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7a28/3813509/63cb918ffc70/rjt03503.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7a28/3813509/0d94a8eea389/rjt03501.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7a28/3813509/0632c1da9dc7/rjt03502.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/7a28/3813509/63cb918ffc70/rjt03503.jpg

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引用本文的文献

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Visual Impairment in Cerebral Venous Thrombosis: The Various Shades of Gray.脑静脉血栓形成中的视力损害:灰色的各种色调
Ann Indian Acad Neurol. 2023 Sep-Oct;26(5):629-630. doi: 10.4103/aian.aian_449_23. Epub 2023 Oct 13.
2
Diagnosis and Treatment of Cerebral Venous Thrombosis: A Review.脑静脉血栓形成的诊断与治疗:综述
Front Aging Neurosci. 2018 Jan 30;10:2. doi: 10.3389/fnagi.2018.00002. eCollection 2018.
3
Spectrum of Visual Impairment in Cerebral Venous Thrombosis: Importance of Tailoring Therapies Based on Pathophysiology.

本文引用的文献

1
Cerebral venous thrombosis presenting with cerebellar ataxia and cortical blindness.小脑共济失调和皮质盲表现的脑静脉血栓形成。
J Stroke Cerebrovasc Dis. 2010 Nov-Dec;19(6):507-9. doi: 10.1016/j.jstrokecerebrovasdis.2009.09.004. Epub 2010 Jun 9.
2
New approaches to visual rehabilitation for cortical blindness: outcomes and putative mechanisms.新方法用于皮质盲的视觉康复:结果和可能的机制。
Neuroscientist. 2010 Aug;16(4):374-87. doi: 10.1177/1073858409356112. Epub 2010 Jan 25.
3
Delay in hospital admission of patients with cerebral vein and dural sinus thrombosis.
脑静脉血栓形成中的视力损害谱:基于病理生理学定制治疗方法的重要性。
Ann Indian Acad Neurol. 2017 Jul-Sep;20(3):294-301. doi: 10.4103/aian.AIAN_11_17.
脑静脉和硬脑膜窦血栓形成患者住院延迟
Cerebrovasc Dis. 2005;19(3):152-6. doi: 10.1159/000083248. Epub 2005 Jan 11.
4
Occipital lobe infarctions: Perimetry and computed tomography.枕叶梗死:视野检查与计算机断层扫描
Neurology. 1981 Sep;31(9):1098-1106. doi: 10.1212/wnl.31.9.1098.
5
Cortical blindness as a manifestation of basilar artery occlusion.
Eur Neurol. 1974;11(1):22-9. doi: 10.1159/000114302.