Nnamdi Ibe Michael Onwuzuruike
Department of Surgery, Consultant Neurosurgeon, Neurosurgical Unit, Ebonyi State University Teaching Hospital, Abakaliki, Ebonyi State, Nigeria.
Niger Med J. 2014 Jan;55(1):73-6. doi: 10.4103/0300-1652.128177.
Myelo-meningoceles are part of congenital afflictions of the spinal column. They arise from the failure of the neural tube to fuse properly during early embryonic growth. The causes and sequalae are multiple and, therefore, require multiple disciplines, to handle them. This study assessed the role of inter-disciplinary approach in the management of myelo-meningoceles.
From 1975 to 2007, the author repaired 20 midline lumbar and lumbo-sacral myelo-meningoceles; 5 in Jamaica and 15 in Nigeria. There were 11 males and 9 females. Their ages, at operation, ranged from 1 to 168 days. All had urine and faecal incontinence and severe paraparesis to paraplegia. Skeletal deformities were present in 16 cases. The operations were carried out under routine general anaesthesia and in prone position. All cases were followed-up for up to 60 months, apart from one who died 4 days at home after discharge.
There were no deaths within the period of hospitalisation, usually about 14 days. Those followed-up have not made much improvement, though they were able to sit up without support and move around by shifting on their buttocks on the floor.
We must continue to help these patients, but under the umbrella of specialised rehabilitation centres with the different specialists working together to make these patients attain a meaningful life and be useful to themselves and the society.
脊髓脊膜膨出是脊柱先天性疾病的一部分。它源于胚胎早期发育过程中神经管未能正常融合。其病因和后果是多方面的,因此需要多学科协作来处理。本研究评估了跨学科方法在脊髓脊膜膨出治疗中的作用。
1975年至2007年,作者修复了20例中线型腰骶部脊髓脊膜膨出;其中5例在牙买加,15例在尼日利亚。患者中男性11例,女性9例。手术时年龄为1至168天。所有患者均有大小便失禁以及严重的下肢轻瘫至截瘫。16例存在骨骼畸形。手术在常规全身麻醉及俯卧位下进行。除1例出院后4天在家中死亡外,所有病例均随访至60个月。
住院期间无死亡病例,住院时间通常约为14天。接受随访的患者虽能在无支撑情况下坐起并通过臀部在地板上移动来四处活动,但改善不大。
我们必须继续帮助这些患者,但要在专门的康复中心的框架下,由不同专科医生共同努力,使这些患者过上有意义的生活,并对自己和社会有所贡献。