卢特巴赫尔氏综合征在农村地区医院的发生：喀麦隆布埃亚的病例报告。
Occurrence of Lutembacher syndrome in a rural regional hospital: case report from Buea, Cameroon.
机构信息
1 Department of Internal Medicine, Faculty of Health Sciences, University of Buea, Buea, Cameroon ; 2 Department of Internal Medicine, General Hospital Douala, Douala, Cameroon ; 3 St Elisabeth Catholic General Hospital, Cardiothoracic Centre, Shisong, Cameroon.
出版信息
Cardiovasc Diagn Ther. 2014 Jun;4(3):263-6. doi: 10.3978/j.issn.2223-3652.2014.06.01.
Abstract
INTRODUCTION
Lutembacher syndrome (LS) is a rare cardiac clinical entity marked by the combination of an atrial septal defect (ASD) and mitral stenosis (MS). Its prognosis is influenced by several factors.
CASE REPORT
We present the case of a young adult male who presented with a 10-month history of exertional dyspnea, orthopnoea, fatigue and cough. Clinical examination revealed features suggestive of advanced congestive heart failure. Echocardiography revealed severe MS and a secundum type ASD with pulmonary hypertension. Patient died on second day of admission.
CONCLUSIONS
LS is a very rare condition. The outcome is better if treated before the onset of heart failure and pulmonary hypertension. However, surgical and percutaneous trans-catheter therapy is costly and not readily available in low-income settings in developing countries.
摘要
简介
卢特巴赫综合征（LS）是一种罕见的心脏临床病症，其特征是房间隔缺损（ASD）和二尖瓣狭窄（MS）同时存在。其预后受多种因素影响。
病例报告
我们报告了一例年轻成年男性病例，其病史为 10 个月的劳力性呼吸困难、端坐呼吸、疲劳和咳嗽。临床检查显示出晚期充血性心力衰竭的特征。超声心动图显示严重的 MS 和继发孔型 ASD 合并肺动脉高压。患者在入院第二天死亡。
结论
LS 是一种非常罕见的病症。如果在心力衰竭和肺动脉高压发生之前进行治疗，预后会更好。然而，手术和经导管介入治疗费用昂贵，在发展中国家的低收入环境中并不容易获得。
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