Prashanthi C, Reddy Sujatha S, Majumdar Kuhu
Department of Oral medicine, Diagnosis and Radiology, M.S.Ramaiah Dental College & Hospital, MSRIT Post, New BEL Road, Bangalore-560054, Karnataka, India; e-mail:
Oral Health Dent Manag. 2014 Sep;13(3):725-7.
Sturge-Weber Syndrome (SWS) is a rare, non-hereditary, congenital neuro cutaneous disorder characterized by vascular hamartomatous proliferations affecting classically, the leptomeninges and the skin of the face and may be associated with glaucoma, seizures and mental retardation. Intraoral findings are variable. A case of Roach type II Sturge Weber syndrome is reported here that did not show any neurological disorder but revealed a prominent angiomatous enlargement of the ipsilateral maxillary gingiva. SWS is a condition where dental management and surgical procedures of the patient can be risky, thus a sound knowledge of the disease and its management protocols better equips the clinician to avoid serious complications.
斯特奇-韦伯综合征（SWS）是一种罕见的、非遗传性的先天性神经皮肤疾病，其特征是血管错构瘤性增生，典型地累及软脑膜以及面部皮肤，可能伴有青光眼、癫痫和智力发育迟缓。口腔内表现各异。本文报告一例Ⅱ型罗奇斯特奇-韦伯综合征病例，该病例未显示任何神经系统疾病，但同侧上颌牙龈出现明显的血管瘤样肿大。SWS是一种患者的牙科治疗和外科手术可能存在风险的疾病，因此，对该疾病及其管理方案有充分的了解能使临床医生更好地避免严重并发症。
