Shaikh Shahid M, Goswami Mousumi, Singh Sanjay, Singh Darrel
Post Graduate Student, Department of Pedodontics & Preventive Dentistry, I.T.S. Dental College, Hospital & Research Center, Greater Noida, India.
Professor and Head, Department of Pedodontics & Preventive Dentistry, I.T.S. Dental College, Hospital & Research Center, Greater Noida, India.
J Oral Biol Craniofac Res. 2015 Jan-Apr;5(1):53-6. doi: 10.1016/j.jobcr.2015.01.002. Epub 2015 Feb 19.
Sturge-Weber syndrome (SWS), also called as encephalotrigeminal angiomatosis is an uncommon congenital neurological disorder & frequent among the neurocutaneous syndromes specifically with vascular predominance. This disorder is characterized by facial capillary malformation & other neurological condition. The oral manifestations are gingival hemangiomatosis restricting to either side in upper and lower jaw, sometimes bilateral. We report a case of SWS with oral, ocular and neurological features.
斯特奇-韦伯综合征(SWS),也称为脑三叉神经血管瘤病,是一种罕见的先天性神经系统疾病,在以血管为主的神经皮肤综合征中较为常见。这种疾病的特征是面部毛细血管畸形和其他神经系统疾病。口腔表现为牙龈血管瘤病,局限于上下颌的一侧,有时为双侧。我们报告一例具有口腔、眼部和神经系统特征的斯特奇-韦伯综合征病例。