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炎性肌成纤维细胞瘤:一种罕见的仅累及胸膜的病例报告。

Inflammatory myofibroblastic tumour: report of a rare form with exclusive pleural involvement.

作者信息

Nobre de Jesus Gustavo, Rocha Sara Lemos, Lopes João Madeira, Santos João Meneses, Oliveira Pedro Soares, Victorino Rui M M

机构信息

Medicina 2, Hospital de Santa Maria/CHLN, Faculdade de Medicina da Universidade de Lisboa, Avenida Egaz Moniz, 1649-035 Lisboa, Portugal.

Departamento de Anatomia Patológica, Hospital da Luz, Avenida Lusiada, 1500-650 Lisboa, Portugal.

出版信息

Case Rep Pulmonol. 2014;2014:621941. doi: 10.1155/2014/621941. Epub 2014 Nov 26.

Abstract

Inflammatory myofibroblastic tumour (IMT) is a rare scleroinflammatory lesion, characterized by a myofibroblastic proliferation with inflammatory infiltrates, with many possible locations and diagnosis based on immunohistochemistry. Pleural IMT is uncommon and is usually an extension of a pulmonary involvement. We report on a 28-year-old woman with a new form of this rare entity, characterized by exclusive pleural involvement.

摘要

炎性肌成纤维细胞瘤(IMT)是一种罕见的硬化性炎性病变,其特征为肌成纤维细胞增生伴炎性浸润,可发生于多种部位,依靠免疫组织化学进行诊断。胸膜IMT较为少见,通常是肺部病变的延伸。我们报告了一名28岁女性,患有这种罕见疾病的一种新形式,其特征为仅累及胸膜。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/18f8/4261844/d71c60cc0404/CRIPU2014-621941.001.jpg

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