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伴进行性吞咽困难的包涵体肌炎:环咽肌切开术治疗

Inclusion body myositis associated with progressive dysphagia: treatment with cricopharyngeal myotomy.

作者信息

Danon M J, Friedman M

机构信息

Department of Pathology, Illinois Masonic Center, Chicago 60657.

出版信息

Can J Neurol Sci. 1989 Nov;16(4):436-8. doi: 10.1017/s031716710002953x.

DOI:10.1017/s031716710002953x
PMID:2553229
Abstract

A 68-year-old man known to have inclusion body myositis underwent a cricopharyngeal myotomy in an attempt to improve his progressive dysphagia. Morphological studies from tissues obtained during this procedure showed the diagnostic features typical of this chronic inflammatory myopathy. To our knowledge this is the first pathological demonstration of inclusion body myositis involving the pharyngeal skeletal musculature.

摘要

一名68岁的已知患有包涵体肌炎的男性接受了环咽肌切开术,试图改善其进行性吞咽困难。在此手术过程中获取的组织的形态学研究显示了这种慢性炎症性肌病的典型诊断特征。据我们所知,这是包涵体肌炎累及咽骨骼肌的首例病理证明。

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