Park So Won, Yi Yoon Young, Han Jung Woo, Kim Heung Dong, Lee Joon Soo, Kang Hoon-Chul
Division of Pediatric Neurology, Department of Pediatrics, Pediatric Epilepsy Clinic, Severance Children's Hospital, Epilepsy Research Institute, Yonsei University College of Medicine, Seoul, Korea.
Department of Pediatrics, Hallym University Kangdong Sacred Heart Hospital, Hallym University College of Medicine, Seoul, Korea.
Korean J Pediatr. 2014 Nov;57(11):496-9. doi: 10.3345/kjp.2014.57.11.496. Epub 2014 Nov 30.
Wernicke's encephalopathy is an acute neurological disorder characterized by mental confusion, oculomotor dysfunction, and ataxia. It has been reported in individuals with alcohol dependence, hyperemesis gravidarum, and prolonged parenteral nutrition without vitamin supplementation. Here we present the case of a 13-year-old male patient with neuroblastoma and a history of poor oral intake and nausea for 3 months. After admission, he showed gait disturbances, nystagmus, and excessive dizziness; his mental state, however, indicated he was alert, which did not fit the classical triad of Wernicke's encephalopathy. A diagnosis of Wernicke's encephalopathy was made only after brain magnetic resonance imaging and serum thiamine level analyses were performed. The patient's symptoms remained after 5 days of treatment with 100-mg thiamine once daily; thus, we increased the dosage to 500 mg 3 times daily, 1,500 mg per day. His symptoms then improved after 20 days of replacement therapy. This case report describes a pediatric patient who was promptly diagnosed with Wernicke's encephalopathy, despite only 2 suspicious symptoms, and who completely recovered after high doses of thiamine were given intravenously.
韦尼克脑病是一种急性神经疾病,其特征为精神错乱、动眼神经功能障碍和共济失调。在酒精依赖者、妊娠剧吐患者以及长期接受肠外营养且未补充维生素的个体中均有相关报道。在此,我们报告一例13岁男性神经母细胞瘤患者,该患者有3个月的口服摄入不良及恶心病史。入院后,他出现步态障碍、眼球震颤和极度头晕;然而,其精神状态显示他神志清醒,这不符合韦尼克脑病的典型三联征。仅在进行脑磁共振成像和血清硫胺素水平分析后才确诊为韦尼克脑病。患者接受每日一次100毫克硫胺素治疗5天后症状仍持续存在;因此,我们将剂量增加至每日3次、每次500毫克,即每天1500毫克。替代治疗20天后他的症状有所改善。本病例报告描述了一名儿科患者,尽管仅有2个可疑症状,但仍迅速被诊断为韦尼克脑病,且在静脉注射高剂量硫胺素后完全康复。