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成人难治性暴发性急性播散性脑脊髓炎(ADEM)

Refractory Fulminant Acute Disseminated Encephalomyelitis (ADEM) in an Adult.

作者信息

Rodríguez-Porcel Federico, Hornik Alejandro, Rosenblum Jordan, Borys Ewa, Biller José

机构信息

Department of Neurology, Loyola University Medical Center, Stritch School of Medicine , Maywood, IL , USA.

Department of Radiology, Loyola University Medical Center, Stritch School of Medicine , Maywood, IL , USA.

出版信息

Front Neurol. 2014 Dec 23;5:270. doi: 10.3389/fneur.2014.00270. eCollection 2014.

DOI:10.3389/fneur.2014.00270
PMID:25566176
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4274983/
Abstract

Acute disseminated encephalomyelitis (ADEM) is characterized by its rapid progression with variable symptoms and severity in adults and children. Multiple therapeutic options have been proposed, but solid evidence is yet to be gathered. We describe an adult man with a fulminant form of ADEM unresponsive to numerous treatment modalities.

摘要

急性播散性脑脊髓炎(ADEM)的特点是在成人和儿童中症状和严重程度各异且进展迅速。虽然已经提出了多种治疗方案,但尚未收集到确凿的证据。我们描述了一名患有暴发性ADEM的成年男性,对多种治疗方式均无反应。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/40df/4274983/8d885a7fdd77/fneur-05-00270-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/40df/4274983/bbf832d19a74/fneur-05-00270-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/40df/4274983/a96b78827656/fneur-05-00270-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/40df/4274983/8d885a7fdd77/fneur-05-00270-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/40df/4274983/bbf832d19a74/fneur-05-00270-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/40df/4274983/a96b78827656/fneur-05-00270-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/40df/4274983/8d885a7fdd77/fneur-05-00270-g003.jpg

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Disease course and outcome of acute disseminated encephalomyelitis is more severe in adults than in children.急性播散性脑脊髓炎的疾病过程和结局在成人中比在儿童中更为严重。
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