Subasioglu Aslı, Savas Selcuk, Kucukyilmaz Ebru, Kesim Servet, Yagci Ahmet, Dundar Munis
Department of Medical Genetics, Izmir Katip Celebi University, Ataturk Training and Research Hospital, Izmir, Turkiye.
Department of Pedodontics, Dentistry Faculty, Izmir Katip Celebi University, Izmir, Turkiye.
Eur J Dent. 2015 Jan-Mar;9(1):153-158. doi: 10.4103/1305-7456.149670.
Supernumerary teeth (ST) are odontostomatologic anomaly characterized by as the existence excessive number of teeth in relation to the normal dental formula. This condition is commonly seen with several congenital genetic disorders such as Gardner's syndrome, cleidocranial dysostosis and cleft lip and palate. Less common syndromes that are associated with ST are; Fabry Disease, Ellis-van Creveld syndrome, Nance-Horan syndrome, Rubinstein-Taybi Syndrome and Trico-Rhino-Phalangeal syndrome. ST can be an important component of a distinctive disorder and an important clue for early diagnosis. Certainly early detecting the abnormalities gives us to make correct management of the patient and also it is important for making well-informed decisions about long-term medical care and treatment. In this review, the genetic syndromes that are related with ST were discussed.
多生牙（ST）是一种口腔牙科学异常，其特征是相对于正常牙列存在过多数量的牙齿。这种情况常见于几种先天性遗传疾病，如加德纳综合征、锁骨颅骨发育不全症以及唇腭裂。与多生牙相关的较罕见综合征有：法布里病、埃利斯-范克里维尔德综合征、南斯-霍兰综合征、鲁宾斯坦-泰比综合征和三指-鼻-指综合征。多生牙可能是一种独特疾病的重要组成部分，也是早期诊断的重要线索。当然，早期检测到这些异常情况能使我们对患者进行正确的管理，对于做出有关长期医疗护理和治疗的明智决策也很重要。在本综述中，讨论了与多生牙相关的遗传综合征。
