Hiraoka Kei, Yamazaki Shigeo, Hosokawa Masao, Suzuki Yasuhiro
Department of Surgery, Keiyukai Sapporo Hospital, Sapporo, Japan
Department of Surgery, Keiyukai Sapporo Hospital, Sapporo, Japan.
J Surg Case Rep. 2015 Apr 23;2015(4):rjv052. doi: 10.1093/jscr/rjv052.
We report a rare case of bronchogenic cyst associated with congenital complete absence of the pericardium. A 17-year-old male was admitted to the hospital for surgical resection of a growing cystic lesion located in the middle mediastinum. The patient was asymptomatic and no significant findings were found on physical examination. Resection of the mediastinal cyst was performed by video-assisted thoracoscopic surgery. The complete absence of the pericardium was immediately observed along with a cystic tumor arising from the mediastinum. After the resection of the cyst, no additional procedure to reconstruct the absence of the left pericardium was performed. Pathological diagnosis was a bronchogenic cyst. Congenital absence of the pericardium may be associated with the bronchogenic cyst and complete absence of the pericardium requires no additional surgical reconstruction, if remaining space in the pleural cavity is small enough to avoid cardiac disposition after surgical resection of the cyst.
我们报告一例罕见的支气管源性囊肿合并先天性心包完全缺如的病例。一名17岁男性因位于中纵隔的一个逐渐增大的囊性病变入院接受手术切除。患者无症状，体格检查未发现明显异常。通过电视辅助胸腔镜手术切除纵隔囊肿。术中立即观察到心包完全缺如，同时有一个源于纵隔的囊性肿瘤。囊肿切除后，未进行额外的重建左心包缺如的手术。病理诊断为支气管源性囊肿。先天性心包缺如可能与支气管源性囊肿相关，如果胸腔内剩余空间足够小，在手术切除囊肿后能避免心脏移位，那么心包完全缺如无需额外的手术重建。
