Swank D W, Hepper N G, Folkert K E, Colby T V
Department of Laboratory Medicine, University of North Dakota, Minot.
Mayo Clin Proc. 1989 Oct;64(10):1264-8. doi: 10.1016/s0025-6196(12)61289-0.
In this report, we describe a case of lymphangiomatosis that mimicked lymphangioleiomyomatosis in a 20-year-old woman. Lung biopsy specimens showed proliferation of anastomosing lymphatic channels in the visceral pleura and dilated peribronchiolar and septal lymphatic channels. During 8 years of follow-up, this process behaved like lymphangioleiomyomatosis with reticulonodular infiltrates and worsening obstructive and restrictive changes evident on pulmonary function tests.
在本报告中，我们描述了一例20岁女性的淋巴管瘤病，其临床表现类似淋巴管平滑肌瘤病。肺活检标本显示脏层胸膜内吻合的淋巴管增生，以及支气管周围和小叶间隔淋巴管扩张。在8年的随访过程中，该病变的表现类似淋巴管平滑肌瘤病，出现网状结节状浸润，肺功能检查显示阻塞性和限制性改变逐渐加重。
