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表现为肠道肿瘤的非分泌型多发性骨髓瘤

Nonsecretory multiple myeloma presenting as an intestinal tumor.

作者信息

Triantafyllopoulou Diana, Mellor Stuart, Cargo Catherine, Gkikas Ioannis, Adiyodi Jagdish, Bin Ayub Ali, Sahasrabudhe Neil, Rokicka Margaret

机构信息

Hematology Department, Royal Blackburn Hospital, Haslingden Road, Blackburn, Lancashire BB2 3HH, UK.

Radiology Department, Royal Blackburn Hospital, Haslingden Road, Blackburn, Lancashire BB2 3HH, UK.

出版信息

Case Rep Hematol. 2015;2015:818715. doi: 10.1155/2015/818715. Epub 2015 Apr 16.

DOI:10.1155/2015/818715
PMID:25960896
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4415489/
Abstract

We report a case of a 43-year-old Caucasian man who presented with colicky abdominal pain and microcytic hypochromic anemia. The patient underwent a colonoscopy where a tumor was seen in the ascending colon; histology showed plasmacytoma of the colon. From the protein electrophoresis, no monoclonal band or free light chains were detected nor was urinary Bence Jones protein present. A bone marrow biopsy showed plasma cell myeloma. To the best of our knowledge, this is the first case of nonsecretory multiple myeloma presenting as plasmacytoma of the colon.

摘要

我们报告了一例43岁的白种男性病例,该患者表现为绞痛性腹痛和小细胞低色素性贫血。患者接受了结肠镜检查,在升结肠发现了一个肿瘤;组织学检查显示为结肠浆细胞瘤。蛋白电泳未检测到单克隆条带或游离轻链,尿本-周蛋白也未检出。骨髓活检显示为浆细胞骨髓瘤。据我们所知,这是首例表现为结肠浆细胞瘤的非分泌型多发性骨髓瘤病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/39bb/4415489/ce5bd433bd8c/CRIHEM2015-818715.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/39bb/4415489/c9f73a26c2d4/CRIHEM2015-818715.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/39bb/4415489/0449d9b78a6a/CRIHEM2015-818715.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/39bb/4415489/ce5bd433bd8c/CRIHEM2015-818715.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/39bb/4415489/c9f73a26c2d4/CRIHEM2015-818715.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/39bb/4415489/0449d9b78a6a/CRIHEM2015-818715.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/39bb/4415489/ce5bd433bd8c/CRIHEM2015-818715.003.jpg

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本文引用的文献

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Non-secretory multiple myeloma relapsing as extramedullary liver plasmacytomas.非分泌型多发性骨髓瘤复发为骨髓外肝浆细胞瘤。
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Aggressive large B-cell lymphoma with plasma cell differentiation: immunohistochemical characterization of plasmablastic lymphoma and diffuse large B-cell lymphoma with partial plasmablastic phenotype.具有浆细胞分化的侵袭性大 B 细胞淋巴瘤:浆母细胞淋巴瘤和具有部分浆母细胞表型的弥漫性大 B 细胞淋巴瘤的免疫组织化学特征。
Haematologica. 2010 Aug;95(8):1342-9. doi: 10.3324/haematol.2009.016113. Epub 2010 Apr 23.
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